Number of the records: 1
Erdheimova-Chesterova choroba
Subject h. Erdheimova-Chesterova choroba Subject h. Erdheim-Chester Disease Entry terms granulomatóza lipidová English X references Granulomatosis, Lipid Scope note in English A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones. subject heading
Number of the records: 1