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skleróza amyotrofická laterálna
Record number d000690 Date 06.06.2025 Type M - MESH Topical term skleróza amyotrofická laterálna Other term English (Pseudonym) ALS - Amyotrophic Lateral Sclerosis
English (Pseudonym) Lou Gehrig Disease
English (Pseudonym) Motor Neuron Disease, Amyotrophic Lateral Sclerosis
Slovak (Pseudonym) ALS - amyotrofická laterálna skleróza
Slovak (Pseudonym) skleróza amyotrofická laterálna, s demenciou
Slovak (Pseudonym) skleróza amyotrofická laterálna, guamská forma
Slovak (Pseudonym) ALS - guamský komplex parkinsonizmus - demencia
Slovak (Pseudonym) skleróza amyotrofická laterálna, guamský komplex parkinsonizmu s demenciou
Slovak (Pseudonym) choroba motorických neurónov, amyotrofická laterálna skleróza
Slovak (Pseudonym) Lou Gehrigova choroba
Slovak (Pseudonym) Gehrigova choroba
Slovak (Pseudonym) choroba guamská
Slovak (Pseudonym) Charcotova choroba
Slovak (Pseudonym) demencia s amyotrofickou laterálnou sklerózou
Slovak (Pseudonym) ALS, guamská forma
UDC C10.228.854.139C10.574.562.250C10.574.950.050C10.668.467.250C18.452.845.800.050 Note A degenerative disorder affecting upper MOTOR NEURONS in the brain and lower motor neurons in the brain stem and SPINAL CORD. Disease onset is usually after the age of 50 and the process is usually fatal within 3 to 6 years. Clinical manifestations include progressive weakness, atrophy, FASCICULATION, hyperreflexia, DYSARTHRIA, dysphagia, and eventual paralysis of respiratory function. Pathologic features include the replacement of motor neurons with fibrous ASTROCYTES and atrophy of anterior SPINAL NERVE ROOTS and corticospinal tracts. (From Adams et al., Principles of Neurology, 6th ed, pp1089-94) subject heading
Number of the records: 1