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kernikterus
Č. záznamu d007647 Dátum 06.06.2025 Typ M - MESH Tematický termín kernikterus Iný termín Angličtina (Pseudonym) Bilirubin Encephalopathy
Angličtina (Pseudonym) Hyperbilirubinemic Encephalopathy
Slovenčina (Pseudonym) žltačka jadrová
Slovenčina (Pseudonym) ikterus jadrový
Slovenčina (Pseudonym) encefalopatia bilirubínová
Slovenčina (Pseudonym) encefalopatia hyperbilirubinemická
MDT C10.228.140.163.480C15.378.295.502C16.614.304.502C18.452.132.480C20.306.502C23.550.429.750 Poznámka A term used pathologically to describe BILIRUBIN staining of the BASAL GANGLIA; BRAIN STEM; and CEREBELLUM and clinically to describe a syndrome associated with HYPERBILIRUBINEMIA. Clinical features include athetosis, MUSCLE SPASTICITY or hypotonia, impaired vertical gaze, and DEAFNESS. Nonconjugated bilirubin enters the brain and acts as a neurotoxin, often in association with conditions that impair the BLOOD-BRAIN BARRIER (e.g., SEPSIS). This condition occurs primarily in neonates (INFANT, NEWBORN), but may rarely occur in adults. (Menkes, Textbook of Child Neurology, 5th ed, p613) predmetové heslo
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